更新于:2025-01-23

Immunoglobulin Light-Chain Amyloidosis

免疫球蛋白轻链淀粉样变性

基本信息

别名
AL、AL AMYLOIDOSIS、AL Amyloidoses
+ [46]
简介
A nonproliferative disorder of PLASMA CELLS characterized by excessive production and misfolding of IMMUNOGLOBULIN LIGHT CHAINS that form insoluble amyloid fibrils (see AMYLOID DEPOSITS) in various tissues. Clinical features include LIVER FAILURE; MULTIPLE MYELOMA; NEPHROTIC SYNDROME; RESTRICTIVE CARDIOMYOPATHY, and neuropathies.

分析

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对领域进行一次全面的分析。
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